NTRK
NTRK abnormalities in NSCLC
TRK oncogene activation through the infusions involving an NTRK 1, NTRK 2 or NTRK3 are commonly observed in solid tumors including non-small cell lung cancer. These gene fusions in non-small cell lung cancer (NSCLC) occur with a frequency of about less than 1%.
NTRK gene fusions can occur in both squamous and non-squamous histology including neuroendocrine carcinomas. It is independent of sex and smoking status. They usually do not occur with other actionable driver mutations. There is seen with a slightly higher frequency in Asian patients.
DNA base sequencing shows an overall sensitivity and specificity of about 81% and 99.9% respectively for the detection of an TRK fusion compared to immunohistochemistry (IHC) which shows an overall sensitivity of 87.9% and specificity of 81%. RNA sequencing provides high sensitivity and specificity. A pattern-TRK IHC can be used as a screening test followed by a confirmatory NGS in positive cases.
Since lung cancer harbors these mutations at a lower frequency, as more recommendations are for screening with IHC first. Because TRK expression is normal and expected in certain organs such as the CNS, IHC positivity can be seen in cancers without TRK fusions. This can include tumors with neuroendocrine differentiation.
Plasma based, cell free DNA assays are not optimal for the detection of an TRK gene fusion.
Drugs
References
Amatu, A. Sartore-Bianchi, K. Bencardino, E.G. Pizzutilo, F. Tosi, S. Siena, Tropomyosin receptor kinase (TRK) biology and the role of NTRK gene fusions in cancer, Annals of Oncology, Volume 30, Supplement 8,2019, Pages viii5-viii15, ISSN 0923-7534,https://doi.org/10.1093/annonc/mdz383.
Solomon JP, Linkov I, Rosado A, Mullaney K, Rosen EY, Frosina D, Jungbluth AA, Zehir A, Benayed R, Drilon A, Hyman DM, Ladanyi M, Sireci AN, Hechtman JF. NTRK fusion detection across multiple assays and 33,997 cases: diagnostic implications and pitfalls. Mod Pathol. 2020 Jan;33(1):38-46. doi: 10.1038/s41379-019-0324-7. Epub 2019 Aug 2. PMID: 31375766
Solomon JP, Hechtman JF. Detection of NTRK Fusions: Merits and Limitations of Current Diagnostic Platforms. Cancer Res. 2019 Jul 1;79(13):3163-3168. doi: 10.1158/0008-5472.CAN-19-0372. Epub 2019 Jun 13. PMID: 31196931.
Drilon A, Tan D S W, Lassen U, Leyvraz S et al. Efficacy and Safety of Larotrectinib in Patients With Tropomyosin Receptor Kinase Fusion–Positive Lung Cancers JCO Precision Oncology 2022 : 6